What a Neurosurgeon Should Know About the Endolymphatic Sac: Part 2 – Diagnosis and Management of the Endolymphatic Sac Tumors

نویسندگان

چکیده

Abstract Objective This article is divided into three parts. In the second part of this review, authors focus on describing endolymphatic sac tumor and presenting illustrative cases. Methods A review previous studies, from 1957 to 2021, basic translational research using human animal (ES) tissue or cells, as well other reviews theme. Results The ES an inner ear structure, which responsible for homeostatic regulation, fluid volume control, immune response etc. One possible alterations ELST, a low-grade malign neoplasm that originates epithelium duct sac. clinical presentation ELST includes hearing loss, tinnitus, headache, vertigo. diagnosis in early stages rare, given group symptoms very similar other, more common, diseases such Meniere syndrome. Its made by computed tomography (CT), magnetic resonance imaging (MRI), immunohistochemistry, confirmed histopathology. However, none these examinations are pathological guidelines ELST. treatment has high rate success. Conclusion difficult due its presentation. Furthermore, interactions between Von Hippel-Lindau disease usually result aggressive condition. Despite difficulty diagnosis, doing it increases chances successful treatment.

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ژورنال

عنوان ژورنال: Arquivos Brasileiros de Neurocirurgia

سال: 2023

ISSN: ['2359-5922', '0103-5355']

DOI: https://doi.org/10.1055/s-0042-1750699